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Gluconeogenesis takes places in what two organs?
Liver and kidney
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Glucose 6 phosphotase is present in what two organs?
Why?
- Liver and Kidney?
- Bc they are responsible for maintaining BSL
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Glucose-6-phosphatase is only present where?
ER of Liver and Kidney
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Even or odd chain fatty acids can enter the TCA cycle?
Odd chain
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How can odd chain fatty acids enter the TCA cycle?
as propionyl coA which is then converted to succinyl-coA
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Hereditary Fructose intolerance is caused by what enzyme deficiency?
Aldolase B
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Hereditary fructose intolerance causes what?
- decrease in P
- decrease in glycogenlysis
- decrease in gluconeogenesis
- hypoglycemia
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Essential fructosuria results from what enzyme deficiency?
how does it present?
- fructokinase
- fructose in urine and blood
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Enzyme deficiency in Classical Galactosemia?
symptom?
- Gal-1 P uridyltransferase
- galacticol..accumulation in lens
- hepatosplenomegaly
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What is sortbitol?
- alcohol version of glucose, fructose or galactose
- Made by alcohol reductase in shwann cells, lens, retina and kidney...those structure dont have sorbitol dyhydrogenase to produce fructose
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What stimulates gluconeogenesis?
- High energy state
- i.e...ATP, Citrate, acetylcoA
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F 1,6 BP and F 2,6 BP stimulate glycolysis or gluconeogenesis
Glycolysis
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What effect does Etoh have on gluconeogenesis?
It inhibits it
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