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foregut structures
lungs, esophagus, stomach, pancreas, liver, gallbladder, bile duct, proximal duodenum
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midgut structures
duodenum distal to ampulla, small bowel, large bowel to distal 1/3 of transverse colon
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hindgut structures
distal 1/3 of transverse colon to anal canal
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definition of low birth weight
<2500g
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definition of premature
<37 weeks
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#1 cause of childhood death
trauma
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pediatric trauma bolus
20cc/kg X2
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best indicator of shock in pediatric patients
tachycardia
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umbilical vessels
3 (two arteries and one vein)
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rule of maintenance IVF in pediatrics
4cc/kg for 1st 10kg, 2cc/kg for next 10kg, 1cc/kg for every add'l kg
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lung tissue with systemic arterial supply and either systemic venous or pulmonary vein drainage
pulmonary sequestration
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intralobar pulmonary sequestration: more typical venous drainage pattern is:
pulmonary veins
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extralobar pulmonary sequestration: more typical venous drainage pattern is:
systemic veins
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disease where cartilage fails to develop in bronchi, leading to air trapping with expiration
congenital lobar overinflation (emphysema)
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lobes most commonly affected by congenital lobar emphysema (2)
RML, LUL
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Structure that communicates with airway, and has poorly-developed alveolar structures
Congenital cystic adenoid malformation
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Extrapulmonary cysts formed from bronchial tissue and cartilage wall
Bronchiogenic cyst
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Treatment of congenital cystic adenoid malformation
Lobectomy
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Treatment of bronchiogenic cyst
Resect cyst
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Most common mediastinal tumor in children
Neurogenic tumors (neurofibroma, neuroganglioma, neuroblastoma)
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Symptoms of mediastinal masses
Respiratory symptoms, dysphagia
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Most common anterior mediastinal tumors (4)
T cell lymphoma, teratoma, thymoma, thyroid cancer
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Most common middle mediastinal tumors (3)
T cell lymphoma, teratoma, cyst (cardiogenic or bronchogenic)
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Most common posterior mediastinal tumors (3)
T cell lymphoma, neuroblastoma, neurogenic tumor
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Risks of choledochal cysts (4)
Cholangiocarcinoma, pancreatitis, cholangitis, obstructive jaundice
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Fusiform dilation of entire CBD, mildly dilated common hepatic duct, normal intrahepatic ducts
Type I choledochal cyst
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Treatment of Type I choledochal cyst
Resection, hepaticojejunostomy
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A true diverticulum off of the CBD
Type II choledochal cyst
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Treatment of Type II choledochal cyst
Resection, hepaticojejunostomy prn
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Dilation of distal intramural CBD involving sphincter of Oddi
Type III choledochal cyst
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Treatment of type III choledochal cyst
Resection, choledochojejunostomy
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Multiple cysts, both intrahepatic and extrahepatic
Type IV choledochal cyst
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Treatment of type IV choledochal cyst
Resection, possible lobectomy
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Intrahepatic cysts with hepatic fibrosis; aka Caroli's disease
Resection, may need lobectomy or transplant
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Most common reason for lymphadenopathy in children
Acute supperative adenitis
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Causes of chronic lymphadenopathy in children (2)
Cat scratch fever, atypical mycoplasma
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Lymphangioma in lateral cervical and submandibular regions in neck predisposed to infection
Cystic hygroma
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Which side is more likely to have congenital diaphragmatic hernia
Left
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Morbidity of CDH
Pulmonary HTN, respiratory compromise
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Most common CDH, located posteriorly on the left
Bochladek's hernia
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Rare CDH located anteriorly
Morgagni's hernia
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Failure of diaphragm to fuse
Eventration
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Internal caving of the sternum, repaired if causing respiratory symptoms for emotional distress
Pectus excavatum
-
Pigeon chest deformity; repaired for emotional distress
Pectus carinatum
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Cyst near angle of mandible; may connect with externial auditory canal and often associated with facial nerve
1st branchial cleft cyst
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cyst on anterior border of SCM muscle; goes through carotid bifurcation into tonsillar pillar
2nd branchial cleft cyst
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most common branchial cleft cyst
2nd
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cyst on lateral neck
3rd branchial cleft cyst
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treament of branchial cleft cyst
resection
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remnant of descent of thyroid gland from foramen cecum
thyroglossal duct cyst
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midline cervical mass that moves with swallowing
thyroglossal duct cyst
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treatment of thyroglossal duct cyst
excision of cyst, tract and hyoid bone
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treatment of hemangiomas
observation, steroids or laser if uncontrollable growth or persistence after age 8
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most common solid abdominal malignancy in children
neuroblastoma
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most common location of neuroblastoma
adrenal glands
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diagnostic studies for neuroblastoma
increased catecholamines, VMA, HVA, and metanephrines
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tumor derived from neural crest cells that is common in the abdomen in children
neuroblastoma
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potential metastases of neuroblastoma and Wilms tumor (2)
lung, bone
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treatment of neuroblastoma
resection , preoperative chemo if needed for clear margins
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stage III neuroblastoma
crosses midline +/- regional nodes
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stage II neuroblastoma
complete excision, does not cross midline
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typically asymptomatic mass that can also present with hematuria or HTN
Wilms tumor
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Main prognostic factor for Wilms tumor
Grade
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Hemihypertrophy, cryptorchidism, Drash syndrome and aniridia
Beckwith-Wiedemann syndrome
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Treatment of Wilms tumor
Nephrectomy, chemotherapy(for stage II +), XRT (for stage III +)
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Stage I Wilms tumor
Limited to kidney, completely excised
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Stage II Wilms tumor
Beyond kidney, completely excised
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Stage III Wilms tumor
Residual nonhematogenous tumor
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Stage IV Wilms tumor
Hematogenous mets
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Stage V Wilms tumor
Bilateral renal involvement
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Most common pediatric malignant liver tumor
Hepatoblastoma
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Tumor marker for hepatoblastoma
AFP
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Histology of hepatoblastoma with best prognosis
Prefetal histology
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Treatment of hepatoblastoma
Resection, downsizing with doxorubicin and cisplatin
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Most common overall children's malignancy
Leukemia (ALL)
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Most common class of solid tumor in children
CNS tumors
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Most common general surgery tumor in children
Neuroblastoma
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Most common general surgery tumor in children under 2
Wilms tumor
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Most common cause of duodenal obstruction in newborns
Duodenal atresia
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Most common cause of duodenal obstruction after the newborn period
Malrotation
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Most common cause of colonic obstruction in children
Hirschprung's
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Most common lung tumor in children
Carcinoid
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Most common cause of painful lower GI bleed in children
Anal fissures
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Most common cause of painless lower GI bleed in children
Meckel's
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Most common cause of upper GI bleed in children <1year (2)
Gastritis, esophagitis
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Most common cause of upper GI bleed in children >1 year to adult (2)
Esophageal varices, esophagitis
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Structure that is a persistant remnant of the vitelline duct
Meckel's diverticulum
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3-12 week old male with projectile vomiting and olive mass: diagnosis?
Pyloric stenosis
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Metabolic derangement in pyloric stenosis
Hypochloremic hypokalemic metabolic alkalosis
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Currant jelly stools and sausage mass in 3month-3 year old: diagnosis?
Intussusception
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Common intussusception lead points in children (3)
Peyer's patches, lymphoma, Meckel's
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Initial treatment for intussusception
Air-contrast enema
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Max pressure with air-contrast enema (or column height)
120mmHg (column height 1 meter)
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newborn with bilious emesis, distension, and lack of meconium: diagnosis?
Intestinal atresia
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Cause of intestinal atresia
Intrauterine vascular accidents
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% of patients with duodenal atresia who also have Down's syndrome
20
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double bubble sign on xray: diagnosis
duodenal atresia
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treatment of duodenal atresia
duodenoduodenostomy or duodenojejunostomy
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proximal esophageal atresia (blind pouch) with distal TE fistula
Type C TEF
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Most common type of TEF
Type C
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Esophageal atresia with no fistula
Type A
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TEF not associated with atresia; most likely to present in adulthood
Type E
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VACTERL: define
Vertebral, anorectal (imperforate anus), cardiac, TE fistula, radius/renal, and limb anomalies
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Treatment of TE fistula
Right extrapleural thoracotomy and primary repair
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Complications of TE fistula repair (5)
GERD, leak, empyema, stricture, fistula
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Sudden onset of bilious vomiting in child: diagnosis?
Malrotation
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Failure of normal counterclockwise 270 degree rotation of small bowel, predisposing to infarction
Malrotation
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Diagnostic finding in UGI for malrotation
Duodenum does not cross midline
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Treatment of malrotation
Resection of Ladd's bands, counterclockwise rotation, cecopexy, duodenum to RUQ, appendectomy
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Symptoms of type C TE fistula (4)
Spitting up feeds, excessive drooling, respiratory symptoms with feeding, unable to place NGT in stomach
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Distal ileal obstruction at birth, causing abdominal distension, bilious vomiting and distended bowel loops. Common in CF
Meconium ileus
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Initial treatment of meconium ileus
Gastrograffin enema or N-acetylcysteine enema
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Bloody stool after first feeding in premature infant: diagnosis?
Necrotizing enterocolitis (NEC)
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Risk factors for NEC (6)
Prematurity, hypoxia, hypotension, anemia, polycythemia, sepsis
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Xray findings in NEC (3)
Pneumatosis, free air, or portal venous air
-
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congenital anomaly presenting with meconium in urine or vagina
imperforate anus
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imperforate anus above levators, with meconium in urine or vagina
high imperforate anus
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imperforate anus below levators
low imperforate anus
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morbidity associated with imperforate anus
constipation, stricture
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congenital anomaly occurring when there is intrauterine rupture of umbilical vein
gastroschisis
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treatment of gastroschisis and omphalocele
resuscitation, place saline-soaked gauzes, repair when stable
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congenital anomaly with bowel exposed to amniotic fluid/air with no sac
gastroschisis
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failure of embryonal development, causing a midline defect
omphalocele
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Cantrell pentalogy of defects
Cardiac, pericardium, sternal cleft, diaphragmatic, omphalocele
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More often associated with congenital anomalies: gastroschisis or omphalocele
Omphalocele
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Most common presenting sign for Hirschprung's
Infants fail to pass meconium in first 24 hours
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Diagnostic test for Hirschprung's
Rectal biopsy
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Failure of neural crest cells to progress in craniocaudal fashion in the bowel
Hirschprung's
-
Surgical treatment of Hirschprungs
Soave, Dulhamel, coloanal anastamosis
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Failure of closure of linea alba
Umbilical hernia
-
Persistent processus vaginalis
Inguinal hernia
-
Most common side for pediatric hernia
Right
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Occurrence of bilateral inguinal hernias in pediatric population
10%
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most common cause of neonatal jaundice requiring surgery
biliary atresia
-
histologic findings of biliary atresia
periportal fibrosis, bile plugging, cirrhosis (late)
-
surgical treatment for biliary atresia
Kasai, liver transplant
-
Time frame within which Kasai must be performed to avoid irreversible liver damage
3 months
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tumor markers for teratoma
AFP, beta-hcg
-
Most common location for teratoma in neonates
Sacrococcygeal
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Treatment of neonatal teratoma
Coccygectomy
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Treatment for undescended testes
Orchiopexy through inguinal incision
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Hypoplasia of abdominal wall, urinary tract abnormalities, bilateral cryptorchidism
Prune belly syndrome
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Most common cause of airway obstruction in infants
Laryngomalacia
-
Symptoms of laryngomalacia
Intermittent respiratory distress, stridor exacerbation in supine position
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Obstruction of choanal opening by bone or mucus membrane
Choanal atresia
-
Treatment of choanal atresia
Surgical correction
-
Most common tumor of the pediatric larynx
Laryngeal papilloma
-
Probable cause of laryngeal papilloma
HPV passed to infant while in birth canal
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