Systemic Pathology - Skin - Peters

  1. Melanocytes are ______ derived cells in ___________ layer, secreting melanin.
    • Neural crest
    • epidermal basal
  2. Melanin is synthesized in _________ catalysed by _____.
    • melanosomes
    • tyrosinase
    • Tyrosine -> DOPA -> -> melanin
  3. Dendritic processes extend between keratinocytes. Melanin is transferred from melanocytes to neighboring keratinocytes in melanosomes.
  4. Innate immune response of skin
    • Immediately defense; short lived; no memory.
    • Physical barriers - skin and mucosal epithelia.
    • Soluble factors - complement, antimicrobial peptides, chemokines, and cytokines.
    • Cells such as monocytes/macrophages, dendritic cells, natural killer cells, and neutrophils.
  5. Adaptive immune response
    Has memory; has specificity; long lasting.
    Initiated by dendritic antigen-presenting cells.
    - ______ cells in epidermis
    - _______ dendritic cells in dermis.
    Executed by T cells and antibodies produced by B cells and plasma cells.
    • Langerhans
    • Dermal
  6. ________ secret cytokines.
    Keratinocytes
  7. Langerhans cells, antigen presenting cells in the epidermis: Phagocytose antigens; migrate via lymphatics to regional lymph nodes; expresses protein on its surface to T lymphocyte then undergo clonal proliferation. Dermal dendritic cells play similar role in the dermis.
  8. Natural Killer (NK) cells
    survey the body looking for transformed or infected cells; kill cells directly or indirectly via the secretion of cytokines.
  9. ________ - Cutaneous immune surveillance in the dermis. ______ function (also _____): take up pathogens, recognize them, and destroy them.
    • Macrophages
    • Phagocytic
    • neutrophils
  10. descriptive terms for various types of skin lesions.
    • Macule
    • Patch
    • Papule
    • Nodule
    • Plaque
  11. Circumscribed flat lesion
    • Macule - 5 mm or smaller in diameter.
    • Patch - > 5mm.
  12. Petechiae
    small (1-2mm) red or purple macules due to minor hemorrahage. Do not blanch with pressure.
  13. Purpura
    • 0.3–1cm red or purple macules and patches.
    • Do not blanch with pressure
  14. Papule
    • Elevated dome-shaped or flat-topped
    • <5 mm
  15. Plaque
    • Elevated flat-topped lesion
    • >5 mm
  16. Vesicle
    • Fluid-filled
    • raised lesion
    • <5 mm
  17. Bulla
    • Fluid-filled .
    • raised lesion .
    • >5 mm.
  18. Pustule
    • Discrete,
    • pus-filled,
    • raised lesion.
  19. Wheal
    • Itchy,
    • transient,
    • elevated lesion,
    • +/-erythema.
    • Dermal edema
  20. Scale
    • Dry,
    • horny,
    • plate like excrescence; Imperfect cornification.
  21. Lichenification
    • thickened and rough skin,
    • prominent skin markings.
    • From Repeated rubbing .
  22. Ulceration
    • Complete loss of the epidermis
    • revealing dermis or subcutis.
  23. Nodule
    >5 mm.
  24. Eschar
    Dead black slouging skin.
  25. Onycholysis
    Nail separates from nail bed.
  26. Microscopic terms
    • Hyperkeratosis-Thickening of the stratum corneum.
    • Basket weave hyperkeratosis
    • Compact Hyperkeratosis.
    • Parakeratosis-Keratinization with retained nuclei in the stratum corneum.
    • Hypergranulosis-Hyperplasia of the stratum granulosum.
    • Spongiosis-Intercellular edema of the epidermis.
    • Hydropic swelling (ballooning) - Intracellular edema of keratinocytes.
    • Acanthosis-Diffuse epidermal hyperplasia with thickening of the malphigian layer.
    • Acantholysis-Loss of intercellular cohesion between keratinocytes.
    • Dyskeratosis-Premature keratinization of cells below the stratum granulosum..
    • Dysplasia-premalignant proliferaton; disorderly, pleomorphic, lacks maturation.
  27. Eczematous dermatitis, clinical and dermatologic findings
    • Acute lesions show erythema and aggregates of tiny pruritic vesicles, which exude clear fluid, and become encrusted.
    • Micro - Spongiosis; vesicles - superficial perivascular dermal lymphocytic infiltrate.
    • Chronic lesions become scaly and thickened (lichenification) from continued scratching.
    • Micro - Acanthosis, hyperkeratosis, dermal scarring.
  28. Eczematous dermatitis, pathogenesis
    Group of disorders of differing etiologies that share similar morphologic and histological features spongioticdermatitis.
  29. Eczematous dermatitis, approach to management
  30. Eczematous dermatitis includes
    • •Dyshidrotic eczyma
    • •Atopic dermatitis
    • •Nummular dermatitis
    • •Contact dermatitis
    • •Photoallergic dermatitis
    • •Drug eruptions.
  31. contact dermatitis, clinical and dermatologic findings
    contact dermatitis, approach to management
  32. contact dermatitis, pathogenesis
    • generic term applied to acute or chronic inflammatory reactions to substances contacting the skin.
    • Two variants:
    • Allergic contact dermatitis - idiosyncratic immunological reaction to an environmental allergen.
    • •Cell-mediated, delayed (type IV) hypersensitivity
    • - reaction mediated by Langerhanscells and t cells.
    • •Ex: Poison ivy; nickel; chromates; synthetic rubber; primula; topical creams.
    • Irritant contact dermatitis follows exposure to physical or chemical substances capable of direct damage to the skin.
    • - Mechanisms include keratin denaturation, removal of surface lipids and water, damage to cell membranes, and direct cytotoxic effects.
    • - Ex: Soaps, detergents, acids and alkalis , industrial solvents.
  33. atopic dermatitis, clinical and dermatologic findings
    • Chronic, relapsing eczematous rash.
    • •Often begins in infancy; Any age.
    • •Infants -head, face, neck, diaper area, and extensor aspects.
    • •Childhood -flexural aspects.
    • •Pruritus is intense -scratching leads to lichenification
  34. atopic dermatitis, pathogenesis
    • Multifactorial disease.
    • •Genetic susceptibility
    • •Abnormal skin barrier function
    • •Abnormal immune system activity
    • •Environmental factors
    • Personal or family history of asthma or allergies.
    • •75% have a family history of atopy.
    • •50% have associated asthma or hay fever.
    • Associated with dry skin (xerosis); Worsens in the winter months.
  35. atopic dermatitis, approach to management
    • Risk of secondary bacterial, dermatophyteand viral infections.
    • The disease improves during childhood; > 50%, clears by teens.
  36. KNOW THIS seborrheic dermatitis, clinical and dermatologic findings
    • A very common chronic dermatosis characterized by redness and scaling where the sebaceous glands are most active: face, scalp, presternal area, body folds.
    • Skin Findings: erythematous or yellowish patches, covered by a greasy scale.
  37. seborrheic dermatitis, pathogenesis
    • Unknown
    • Presents in infants; Second peak in adults.
    • Male predominance; Often a family history.
    • Linked with the yeast Malessezia, immunologic abnormalities, sebaceous activity, stress, neurological disorders, and AIDS.
    • Course: Self-limited with a good prognosis in infants: Chronic and relapsing in adults
  38. KNOW THIS erythema multiforme, clinical and dermatologic findings
    • An acute, self-limited, usually mild, often relapsing mucocutaneoussyndrome characterized by presence of target-shaped plaques with or without central blisters, predominantly on face and extremities.
    • Skin Findings:
    • Target lesions, macules, papules, vesicles, bullae.
    • •Symmetric; extremities, arms, legs, hands, feet, anywhere.
    • •Half have oral or vermillion border lesions.
    • •EM minor -No mucosal involvement.
    • •EM major -Mucosal involvemenet.
  39. erythema multiforme, pathogenesis
    • Cell-mediated cytotoxic reaction.
    • •Immunologic response, most often, to a recurrent herpes simplex virus infection.
    • •Begins a week after a recurrence of herpes.
    • •Also M. pneumoniae, other infections, drugs, neoplasia.
    • Any age, peaks in 20-40s ; children.
  40. Stevens-Johnson syndrome/toxic epidermal necrolysis, clinical and dermatologic findings
    • Acute, life-threatening skin and mucous membrane reaction characterized by extensive necrosis and detachment of the epidermis.
    • •Previously considered severe variants of erythema multiformenow considered a separate entity.
    • SJS and TEN same process; Vary in % of involved surface area.
    • •Stevens-johnsonsyndrome -involved area < 10% body surface.
    • •SJS/TEN overlap 10% -30%;
    • •Toxic epidermal necrolysis> 30%;
  41. Stevens-Johnson syndrome/toxic epidermal necrolysis, pathogenesis
    Stevens-Johnson syndrome/toxic epidermal necrolysis, approach to management
  42. lichen planus,
    • clinical and dermatologic findings
    • pathogenesis
    • approach to management
  43. psoriasis.
    • clinical and dermatologic findings
    • pathogenesis
    • approach to management
Author
neopho
ID
326198
Card Set
Systemic Pathology - Skin - Peters
Description
Systemic Pathology - Skin - Peters
Updated