-
midgut returns to abdomen by
-
three layers of embryo disk
-
which umbilical vein atrophies
-
three most common wall defects
- gastrochisis
- omphalocele- umb hernia
-
prevelence of omphalocele
1 in 4000
-
prevalence of gastroschisis
12 per 10,000
-
which omp or gast has membrane
omph
-
gast is found on which side of chord
right
-
what organ is almost never in gast
liver
-
which has associated anomolies gast or omph
omph
-
what is the membrane of omph
amnion and peritoneum
-
two types of omph
- 1- contain liver
- 2- bowel without liver (higher risk for aneuploidy)
-
prognosis for omph
- depends on defect and structures and chrom anom
- 80% with more than one abnormality
- without other anom 10% mortality
-
omph sonographic features
- involvement of umb cord
- ascites
- hydraminos (1/3)
- omph may occur with hernia
- chrom anom in 35-60% omph
-
gastroschisis
- umb wall defect to right of umb cord
- herniation of bowel no membrane- can be other org (no liver)
- thought to be consequence of right umb vein atrophy
- 2-4cm defect
- next to cord insertion
-
omph or gast AFP levels higher
gast
-
-
which is more prevelent gast or omph
omph
-
ischemia
- compression of mesenteric vessles or bowel torsion
- can get gangrene bowel or perforation
-
prognosis for uncomplicated gastrosch
- excellent
- surgical repair in hrs of delivery
-
when can you detect gastroch
- 12 weeks
- high afp
- free floating bowel
-
amniotic band syndrome
ruptue of amnion which leads to entrapment or entaglement of fetal parts by sticky chorion
-
early entrapment amniotic band
- craiofacial defects
- internal malformations
-
late entrapment amniotic band
amputation of limb restrictions
-
prevelance of amniotic band synd
7.8 in 10,000
-
beckwith- widemann syndrome
- rare group of disorders with omphalocele, macroglossia, viseromegaly
- can have embryonic tumors (Wilms, hepatoblastoma, neuroblastoma)
- macrosomia
- 3rd tri polyhydraminos
-
bladder exstrophy
lower structures protrude (bladder)
-
cloacal exstrphy
two hemibladders seperated by intestinal mucosa and are extrophied
-
pentalogy of cantrell
- rare cleft of distal sternum, midline ant wall, internal
- cardiac defect
- high or super umb omphalocele
- mayhave heart displacement
-
ectopic cordis
- heart outside chest through sternum
- cleft sternum
-
limb body wall complex
- death
- large cranial defect
- facial cleft
- body defect (abdomen thorax limb)
- may have scoliosis
- when fusion of amnion and chorion- amnion doesnt cover umb cord but is a sheet cont with body and placenta
- short cord adhered to placenta
-
which sid more common with limb body
left 3xs more common
|
|
